How is amino acid urine disease to return a responsibility?

summary

Amino aciduria is a kind of metabolic disease characterized by excessive excretion of amino acids in urine, which can be divided into prerenal, renal and mixed. All kinds of high amino acid urine disease treatment effect is very different, some through strict control of the diet of the corresponding amino acid intake or supplement some vitamins, amino acid urine disease is how to return a responsibility? Next, I'd like to share my views with you.

How is amino acid urine disease to return a responsibility?

"Prerenal" amino acid urine: ① "spillover" amino acid urine: such as phenylpyruvic aciduria, maple juice urine, is caused by a certain amino acid metabolism defect. ② "Competitive" amino acid urine: such as hyperprolinemia, etc., is caused by competition with amino acids in the same transport system in renal tubules.

Renal "amino acid urine": it is caused by the defect of proximal convoluted tubule transport. ① Single group amino acid transport system defect: that is, the transport system defect of proximal renal tubule to a certain group of amino acids, which makes the group of amino acids excreted from urine, including lysine, arginine, ornithine, cystine, proline, hydroxyproline, glycine, aspartate, glutamate, etc. ② Multiple defects of amino acid transport system: due to multiple functional defects of proximal convoluted tubule, multiple amino acid urine, accompanied by diabetes, hyperphosphatemia, uric acid dysfunction, such as Fanconi syndrome, Lowe syndrome, etc.

The total excretion of amino acids in urine is increased or the excretion of individual amino acids is significantly increased, which is called amino acid urine. Amino acid is an important nutrient in human body, most of which can be used to synthesize protein. The amino acids in plasma can be filtered out to the original urine freely through the glomerulus, and most of them can be reabsorbed back to the blood through the proximal renal tubules.

matters needing attention

Once suffering from amino acid urine, must strictly control diet, usually to supplement some vitamins, to eat more fresh vegetables and fruits to goods, good effect also need to take various measures.