How is infantile congenital pachyonychia treated?

summary

Pachyonychia congenita is a rare hereditary skin disease with hypertrophic nail. It was first named by Jadassohn and lewandowsky in 1906. It is usually divided into four types, type I is the most common, type IV is also known as delayed congenital pachyonychia. How is infantile congenital pachyonychia treated? Next, I'd like to share my views with you.

How is infantile congenital pachyonychia treated?

The removal of thick nail can only relieve the symptoms temporarily. Removal of nail matrix is not beneficial to the curative effect. However, curettage of nail matrix and nail bed is a simple and effective treatment. Keratolytic agents can be used locally in keratotic lesions,

Such as lactic acid lotion, salicylic acid and urea preparation. Oral retinoic acid (isoretinoic acid) can clear keratotic papules and leukoplakia, but it has no effect on palmoplantar keratosis.

After the nail bed curettage, we should pay special attention to the diet, try not to eat fish, shrimp, crab and other fishy smell, can't eat peanuts, soybeans and other food, and it's better not to use peanut oil when cooking to avoid wound suppuration and infection.

matters needing attention

At ordinary times, we should pay special attention to the diet. First of all, seafood must not be eaten, and spicy food should be less touched, and try not to eat fish, shrimp and crab.