Fetal Hirschsprung's disease?

summary

Hirschsprung's disease of the newborn, also known as intestinal agangliosis, is caused by the continuous spasm of the rectum or the distal colon and the fecal congestion of the proximal colon, which makes the intestine hypertrophy and expansion. It is a common congenital intestinal malformation in children. Let's talk about the symptoms of fetal megacolon?

Fetal Hirschsprung's disease?

Delayed fecal excretion: 90% of the cases had no fecal excretion or very little fecal excretion at birth. After the feces were discharged, the symptoms were relieved, and constipation recurred several days later.

2. Abdominal distension: 80% of the cases showed full abdominal distension, severe abdominal distension cases showed intestinal shape. Vomiting: vomiting and abdominal distension occurred in 60% of cases. The more severe constipation, the more frequent vomiting.

3. * complication: Hirschsprung's disease and colitis in the newborn. Intestinal perforation is the most serious complication, and there is a long term retention of feces, intestinal wall circulations and bacteria in the colon. In addition, the neonatal intestinal wall is thin, the pressure in the intestinal cavity is increased, and the part with the greatest pressure is easy to cause perforation.

matters needing attention

(1) Early performance for low acute intestinal obstruction symptoms, after the birth of the sick child, there is a history of delayed fecal discharge, abdominal distension, vomiting, anal examination or enema can only be discharged feces, and symptoms relieved. Later, abdominal distension and constipation should be considered（ 2) X-ray examination: abdominal plain film in upright position and barium enema examination showed that the intestinal cavity was generally flatulent, with fluid level and dilated intestinal loop. Barium enema showed that the colonic wall of the spasmodic segment disappeared in the form of a pouch, and became flat without peristalsis. The rectum and the distal part of sigmoid colon were narrow and thin, and the proximal part of sigmoid colon and descending colon were dilated obviously. After 24 hours, barium remained.