Familial amyloid polyneuropathy?

summary

This disease includes many clinical types, mainly according to the race of the family. In recent years, with the development of molecular biology, gene mutations can be classified according to their characteristics. The corresponding relationship between the two classifications is shown in Table 1. FAP is autosomal dominant inheritance, but the clinical characteristics of different types are different. Let's share my experience with you.

Familial amyloid polyneuropathy?

Eat more lecithin containing foods, such as egg yolk, soybean, fish head, sesame, mushroom, yam and black fungus, Cereals, small fish, animal liver, eel, red bellied snake, etc. Lecithin can protect and repair nerves.

General patients should eat more sweet and warm tonic food, such as millet, jujube, hawthorn, Shantao, angelica, adzuki bean, lotus seed, raisin, walnut kernel, ginger, beef, mutton, black chicken, etc., which is most conducive to enhance their own immunity and help the recovery of the disease. Sweet food can play the role of tonifying, harmonizing and delaying. Therefore, it can nourish and strengthen the body, regulate the five internal organs, Qi, blood, yin and Yang, and any deficiency.

Avoid coffee and other exciting drinks. Damp heat syndrome avoid spicy, warm food, such as wine, pepper, dried ginger, pepper, cinnamon and so on. Don't smoke or drink. There is no effective prevention method. Strengthening the nursing and symptomatic treatment of the patients can prolong the survival period.

matters needing attention

Different types of systemic involvement may have different manifestations. There may be endocrine gland dysfunction, hepatosplenomegaly, proteinuria or nephropathy, abnormal globulinemia, chronic glaucoma and megaglossia. FAP usually progressed slowly and eventually died due to multiple organ involvement. Primary amyloid neuropathy progressed rapidly and had a poor prognosis. The patients died within 2-10 years after onset, with an average survival of 1-2 years.