Juvenile macular dystrophy symptoms?

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Recessive macular dystrophy, also known as yellow macular fundus with macular degeneration (stargardts disease). It is a primary autosomal recessive disease in the retinal pigment epithelium. Juvenile macular dystrophy symptoms? Let's talk about it

Juvenile macular dystrophy symptoms?

The fundus is completely normal, but the central visual acuity has decreased obviously, so it is easy to be misdiagnosed as amblyopia or hysteria. If you give FFA examination at this time, you can see a large number of small weak fluorescent spots. So FFA is very important for the early diagnosis of this disease.

The earliest fundus changes were the disappearance of central reflection, and then the small gray yellow spots were seen in the deep layer of the macula, and gradually formed a transverse oval atrophy area with a clear boundary, with a transverse diameter of 1.5-2pd and a diameter of 1.0-1.5pd, showing the appearance of a hammered bronze atrophic area. During the course of the disease, yellow spots appear around the atrophic area, and the atrophic area expands, so it develops very slowly and continuously, and can invade the whole posterior pole, but generally not beyond the range surrounded by the central retinal artery and vein of the upper and lower temporal sides, let alone reaching the equator. At this time, FFA showed mottled strong fluorescence in the whole atrophic area, and there were small insect like fluorescence spots around it corresponding to the yellow spots. The mottled and wormhole like fluorescent spots are a kind of transparent fluorescence due to the damage of pigment epithelium.

In the macular region, choroidal vessels were found to be sclerotic and atrophic, with irregular pigmented spots, indicating that choroidal capillaries had also been damaged. Irvine et al. Speculated that the damage was secondary, which was a disuse atrophy due to the long-term loss of function and metabolism of the outer layer of retinal neuroepithelial layer and suprapigmented cortex.

matters needing attention

Dietary taboo: 1, avoid beans, peanuts, corn and other hard food difficult to digest. 2. Avoid fried, fried, smoked, baked and fat, too sweet food. 3. Avoid sesame, sesame oil, green onion, ginger and all kinds of flavoring with strong aroma.