How is infantile myofibromatosis treated?

summary

Infantile myofibromatosis, also known as congenital generalized fibromatosis, is uncommon and occurs more frequently in male infants. This disease is characterized by multiple solid dermis and subcutaneous nodules. It occurs at birth or shortly after birth, especially in the head, neck and trunk. How is infantile myofibromatosis treated? Let's talk about it

How is infantile myofibromatosis treated?

It is characterized by multiple solid dermis and subcutaneous nodules. It occurs at birth or shortly after birth, and most frequently occurs in the head, neck and trunk. Bone damage occurred in 50% of the patients. If fibroma only occurs in skin and bone, the prognosis is good. If there is no complication, the fibroma will subside naturally in 1-2 years old.

Fibroma may invade viscera, including gastrointestinal tract, breast, lung, liver, pancreas, tongue, serosa, lymph node or kidney. The mortality rate of this kind of extensive damage is high, up to 80%. The damage can subside naturally if it survives for more than 4 months.

Single myofibroma is a single subcutaneous nodule or mass, common in the head, no visceral damage, rare recurrence. The subcutaneous nodules in the cell area showed oval to spindle shaped fibroblasts arranged in fascicles or vortices. In the area with few cells, the stroma showed mucoid and capillary hyperplasia.

matters needing attention

Should be light, eat more fruits and vegetables, reasonable diet, pay attention to adequate nutrition. Avoid alcohol and tobacco, avoid spicy. Avoid greasy, avoid alcohol and tobacco. Avoid cold and raw food. Should eat high protein nutritious food, rich in vitamins and cellulose, reduce the production of intestinal ammonia, alleviate or prevent the occurrence of hepatic encephalopathy.