What does 8-year-old child suffer from phenylketonuria to eat

summary

Phenylketonuria is a kind of hereditary disease, so when a child's parents or grandparents have phenylketonuria, the child needs to pay attention and check whether he has this congenital disease. Let's talk about what 8-year-old children eat when they suffer from phenylketonuria.

What does 8-year-old child suffer from phenylketonuria to eat

First: a low phenylalanine diet. It is mainly suitable for typical PKU and blood phenylalanine continuously higher than 1. 22 mmol / L (20 mg / dl). Because phenylalanine is an essential amino acid for protein synthesis, complete lack of phenylalanine can also lead to nervous system damage. Therefore, special low phenylalanine milk powder can be fed to infants, and low protein foods such as starch, vegetables and fruits should be used as supplementary food in early childhood.

Second: the purpose of dietary therapy is to keep phenylalanine in the blood at 0. 24～0。 6 mmol / L, children can be in low phenylalanine food feeding on the basis of supplemented with breast milk and milk. It contains about 40mg phenylalanine per 100ml breast milk and 50mg per 30ml milk. The special food that limits the intake of phenylalanine is expensive and difficult to operate.

Third: in addition, some children with phenylketonuria are not caused by the lack of phenylalanine hydroxylase activity, but by the lack of tetrahydrobiopterin, so they need to take tetrahydrobiopterin treatment, and do not need special milk powder treatment. However, tetrahydrobiopterin deficiency can cause neurotransmitter deficiency at the same time, so 5-hydroxytryptamine and levodopa should be given at the same time.

matters needing attention

For patients with phenylketonuria, in addition to the corresponding treatment, through the above food adjuvant treatment is also good, if you want to let the child's disease get better treatment, the best way is to be able to discover the disease and treat the disease as soon as possible.